tyrosinemia

[ tahy-roh-si-nee-mee-uh, tir-oh- ]
/ ˌtaɪ roʊ sɪˈni mi ə, ˌtɪr oʊ- /

noun Pathology.

an inherited disorder of tyrosine metabolism that can lead to liver and kidney disease and mental retardation unless controlled by a special diet.

Origin of tyrosinemia

First recorded in 1960–65; tyrosine + -emia

Words nearby tyrosinemia

Medical definitions for tyrosinemia

tyrosinemia
[ tī′rə-sĭ-nēmē-ə ]

n.

An inherited disorder of tyrosine metabolism marked by an increase in the concentration of tyrosine in the blood, an increase in urinary excretion of tyrosine and related compounds, hepatosplenomegaly, nodular cirrhosis of the liver, multiple renal tubular reabsorptive defects, and vitamin D-resistant rickets.