Maroteaux-Lamy syndrome

[ măr′ə-tōlä-mē, mä-rô- ]

n.

An inherited defect in mucopolysaccharide metabolism characterized by excretion of dermatan sulfate in the urine, retarded growth, lumbar kyphosis, sternal protrusion, knock-knee, and usually enlargement of the liver and spleen. type VI mucopolysaccharidosis

Words nearby Maroteaux-Lamy syndrome