alkaptonuria

[ al-kap-tuh-noo r-ee-uh, -nyoo r- ]
/ ælˌkæp təˈnʊər i ə, -ˈnyʊər- /

noun Pathology.

excessive excretion of homogentisic acid in the urine, caused by a hereditary abnormality of the metabolism of tyrosine and phenylalanine.

Origin of alkaptonuria

First recorded in 1885–90; alkapton + -uria

Medical definitions for alkaptonuria

alkaptonuria

n.

An inherited disorder that affects phenylalanine and tyrosine metabolism and leads to the excretion of homogentisic acid in the urine. homogentisuria